Understanding Cystic Fibrosis
Unlike other chronic lung diseases such as COPD, cystic fibrosis isn’t a disease that develops over time. Instead it is a lifelong, hereditary disease that affects your lungs, pancreas and other vital organs due to thick and sticky secretions.
The secretions are thin and slippery like a lubricant in a healthy patient, but a defective gene causes mucus and digestive juices to become thick and sticky.
Resulting in clogged airways and digestive passageways. When cystic fibrosis (CF) was first being diagnosed during the 1950’s, patients rarely reached the age to go to elementary school.
Progress is shown in treatments as in 1985 the average lifespan of patients was 25. As short ago as 2007 the diagnosis of cystic fibrosis meant patients still had a limited life span, but with cutting edge research efforts doctors have been able to extend the life expectancy of patients dramatically to a median age of 40.7 (cff.org).
With proper treatment and disease education, patients can still attend school, work and have a high quality personal life.